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VOLUME 7 , ISSUE 2 ( July-December, 2015 ) > List of Articles


Hereditary Dystrophic Epidermolysis Bullosa A Rare Case Report

Shagun Sinha

Citation Information : Sinha S. Hereditary Dystrophic Epidermolysis Bullosa A Rare Case Report. CODS J Dent 2015; 7 (2):84-86.

DOI: 10.5005/cods-7-2-84

License: CC BY-NC-ND 3.0

Published Online: 01-12-2017

Copyright Statement:  Copyright © 2015; The Author(s).


Epidermolysis bullosa (EB) is a diverse group of disorders characterized by blister formation with tissue separation occurring at variable depths in the skin and oral mucosa depending on the specific EB type. Oral tissue fragility and blistering is common to all EB types. However oral debilitation as a result of soft tissue scarring is primarily limited to the recessive dystrophic EB subtypes. Due to extreme mucosal fragility such patients are managed by modified dental care practices. This case report describes a rare case of recessive dystrophic EB.

How to cite this article: Neena IE, Sinha S, Poornima P, Pallavi Urs. Hereditary Dystrophic Epidermolysis bullosa- A Rare Case Report. CODS J Dent 2015;7: 84-86

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